Bart’s syndrome (also called aplasia cutis congenita type VI) is a genetic disease characterized by aplasia cutis congenita, epidermolysis bullosa and dystrophic nails. Localized skin defects are thought to be caused by bullous lesions which may occur during intrauterine period. We have presented a case that found skin defects in both ankle and back of the foot immediately after birth. Our patient developed bullous lesions in areas exposed to the pressure on the postnatal third day. He was diagnosed with Bart’s syndrome with family history and distrophic changes in the nails. In the following days, the skin lesions improved with conservative treatment (topical antibacterial ointment and wet gauze dressing). The patient was discharged on the postnatal 30^th day. It was informed that the patient died on postnatal 57^th day who was never brought to clinical controls.