A case of successful a single stage repair of aortic coarctation and ascending aortic aneurysm in a 26-year-old man is presented. He was referred to our clinic due to chest pain. Because echocardiography had showed aneurysmatic ascending aorta and there was no distal peripheral arterial pulses, computed tomography was made. The computed tomography demonstrated giant ascending aorta and distal aortic coarctation. We performed Bentall procedure for ascending aorta and coarctation repair at single operation with two different incisions. At the one year follow-up, he was free of complications and two-dimensional echocardiography revealed normal heart contractility, good function of the aortic valvular prosthesis, a regular ascending aorta, and no evidence of aneurysm.